Literature database

Intravenous gamma-globulin therapy in Diamond-Blackfan anemia.

Intravenous gamma-globulin therapy in Diamond-Blackfan anemia.

Sumimoto S, Kawai M, Kasajima Y, Hamamoto T.
Acta Paediatr Jpn. 1992 Apr;34(2):179-80.


Department of Pediatrics, Sumitomo Hospital, Osaka, Japan.

Pure red cell aplasia (PRCA) is a rare disorder of erythrocyte production which is believed to have an autoimmune basis in most cases. Diamond-Blackfan anemia (DBA) is one type of congenital PRCA. Since PRCA has been reported to respond to intravenous gamma-globulin (IVGG) therapy, we administered IVGG to a 2 year old girl with DBA resistant to corticosteroids and observed slight therapeutic effect.

Publication Types:
  • Case Reports

PMID: 1621524 [PubMed - indexed for MEDLINE]